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PGC-1α, mitochondrial dysfunction,and Huntington's disease
Institution:1. Department of Biology, University of Copenhagen, Denmark;2. Core Facility for Integrated Microscopy, Department of Biomedical Sciences, University of Copenhagen, Denmark;1. Department of Neurology, Ulm University, DE 89081, Germany;2. Institute of Anatomy and Cell Biology, Ulm University, Ulm, DE 89081, Germany;3. Department of Gene Therapy, Ulm University, Ulm, DE 89081, Germany;4. Genomics Core Facility, Ulm University, Ulm, DE 89081, Germany;5. INSERM U1118, F 67085, France;6. Université de Strasbourg, fédération de Médecine Translationnelle, F 67085, France;7. Department of Neurodegenerative Disorders and Gerontopsychiatry, University of Bonn, 53127 Bonn, Germany
Abstract:
Keywords:PGC-1α  PPARs  SIRT1  SIRT3  Mitochondrial dysfunction  Huntington's disease  Oxidative stress  Energy metabolism  Mitochondrial dynamics  Mitophagy  Neurodegeneration  Therapeutics
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