Topical Enzyme-Replacement Therapy Restores Transglutaminase 1 Activity and Corrects Architecture of Transglutaminase-1-Deficient Skin Grafts |
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Authors: | Karin Aufenvenne,Fernando Larcher,Ingrid Hausser,Blanca Duarte,Vinzenz Oji,Heike Nikolenko,Marcela Del  Rio,Margitta Dathe,Heiko Traupe |
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Affiliation: | 1 Department of Dermatology, University Hospital Münster, 48149 Münster, Germany;2 Epithelial Biomedicine Division, Centro de Investigaciones Energéticas, Medioambientales, y Technológicas and Centro de Investigación Biomédica en Red de Enfermedades Raras, 28040 Madrid, Spain;3 Department of Dermatology, University Hospital Heidelberg, 69120 Heidelberg, Germany;4 Electron Microscopy Core Facility, Heidelberg University, 69120 Heidelberg, Germany;5 Institute of Pathology, University Hospital Heidelberg, 69120 Heidelberg, Germany;6 Leibniz Institute of Molecular Pharmacology, 13125 Berlin, Germany;7 Biomedical Engineering Department, Universidad Carlos III de Madrid, 28040 Madrid, Spain |
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