Procollagen with skipping of alpha 1(I) exon 41 has lower binding affinity for alpha 1(I) C-telopeptide, impaired in vitro fibrillogenesis, and altered fibril morphology. |
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Authors: | Wayne A Cabral Andrzej Fertala Laura K Green Jarmo Korkko Antonella Forlino Joan C Marini |
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Institution: | Section on Connective Tissue Disorders, Heritable Disorders Branch, NICHD, National Institutes of Health, Bethesda, Maryland 20892, USA. |
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