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Enhancing Autophagy with Drugs or Lung-directed Gene Therapy Reverses the Pathological Effects of Respiratory Epithelial Cell Proteinopathy |
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| Authors: | Tunda Hidvegi Donna B Stolz John F Alcorn Samuel A Yousem Jieru Wang Adriana S Leme A McGarry Houghton Pamela Hale Michael Ewing Houming Cai Evelyn Akpadock Garchar Nunzia Pastore Patrizia Annunziata Naftali Kaminski Joseph Pilewski Steven D Shapiro Stephen C Pak Gary A Silverman Nicola Brunetti-Pierri David H Perlmutter |
| Abstract: | |
| Keywords: | autophagy chronic obstructive pulmonary disease (COPD) protein misfolding proteostasis pulmonary fibrosis α 1antitrypsin deficiency misfolded α 1antitrypsin |