Langerhans cell histiocytosis: report of a single organ involvement in a child |
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Authors: | Buza Natalia Lagarde D C Dash Srikanta Haque Salima |
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Institution: | Department of Pathology and Laboratory Medicine, Tulane University Health Sciences Center, New Orleans, LA 70112-2699, USA. |
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Abstract: | Langerhans cell histiocytosis is a rare disorder characterized by abnormal proliferation of Langerhans cells that can affect various organ systems. The disease usually presents as a unifocal lytic bone lesion and can affect any age group. Less frequently it presents as a disseminated disease with multisystem involvement. Hepatic manifestation in Langerhans cell histiocytosis is relatively rare and usually presents as a part of a disseminated process. We report a case of Langerhans cell histiocytosis involving only the liver in a 9-years-old child. |
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Keywords: | Langerhans cell histiocytosis histiocytosis X liver sclerosing cholangitis |
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