烟雾病5例临床分析

目的：研究烟雾病（moyamoya disease,MMD）的临床及影像学特征。方法：回顾性分析5例烟雾病患者,分析其临床及影像学特点。结果：本组病例既往均无阳性病史,中、青年起病,男性居多,均以缺血性脑血管病起病,肢体瘫痪不重,经颅多普勒（TCD）及头颅核磁改变明显,数字减影血管造影（DSA）检查均存在血管闭塞及侧支开放,烟雾血管网形成,1例MRA证实烟雾血管网形成。结论：对于无既往史的中、青年脑卒中患者,要考虑MMD的可能,需完善TCD、头核磁检寻找证据,最后完善数字减影血管造影确诊。

Clinical Analysis of 5 Cases of Moyamoya Disease

Objective：To study the clinical and radiological features of the moyamoya disease（moyamoya disease,MMD）.Methods：We retrospectively analysed 5 cases of moyamoya disease,and observed the clinical and radiographic features of the patients.Results：All cases for medium or youth onset,male predominance,all with ischemic cerebrovascular disease onset,hemiparesis,not heavy,head MRI and TCD change significantly.5 patients with DSA check there are occlusion of the blood vessel and collateral open,smoke vessels network forming.1 case confirmed with MRA.Conclusions：The middle-aged and young stroke patients without past history should be confirmed as MMD by improving the TCD,head magnetic resonance imaging examination and digital subtraction angiography.