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The oxidoreductase PYROXD1 uses NAD(P)+ as an antioxidant to sustain tRNA ligase activity in pre-tRNA splicing and unfolded protein response
Authors:Igor Asanović  Emilia Strandback  Alena Kroupova  Djurdja Pasajlic  Anton Meinhart  Pai Tsung-Pin  Nemanja Djokovic  Dorothea Anrather  Thomas Schuetz  Marcin Józef Suskiewicz  Sirelin Sillamaa  Thomas Köcher  Rebecca Beveridge  Katarina Nikolic  Alexander Schleiffer  Martin Jinek  Markus Hartl  Tim Clausen  Javier Martinez
Institution:1. Max Perutz Labs, Medical University of Vienna, Vienna BioCenter (VBC), Dr. Bohr-Gasse 9/2, 1030 Vienna, Austria;2. Institute of Biochemistry, Graz University of Technology, Petersgasse 12/2, 8010 Graz, Austria;3. Department of Medical Biochemistry and Biophysics, Karolinska Institutet, 171 77 Stockholm, Sweden;4. Department of Biochemistry, University of Zurich, Winterthurerstrasse 190, 8057 Zurich, Switzerland;5. Research Institute of Molecular Pathology (IMP), Vienna BioCenter (VBC), Campus-Vienna-BioCenter 1, 1030 Vienna, Austria;6. Institute of Molecular Biotechnology of the Austrian Academy of Sciences (IMBA), Vienna BioCenter (VBC), Dr. Bohr-Gasse 3, 1030 Vienna, Austria;7. AnnJi Pharmaceutical, Taipei, Taiwan;8. Department of Pharmaceutical Chemistry, Faculty of Pharmacy, University of Belgrade, Vojvode Stepe 450, 11221 Belgrade, Serbia;9. Max Perutz Labs, University of Vienna, Vienna BioCenter (VBC), Dr. Bohr-Gasse 9, 1030 Vienna, Austria;10. Department of Internal Medicine III (Cardiology and Angiology), Medical University of Innsbruck, Anichstraße 35, 6020 Innsbruck, Austria;11. Sir William Dunn School of Pathology, University of Oxford, South Parks Road, OX1 3RE Oxford, UK;12. Institute of Molecular and Cell Biology, University of Tartu, Riia 23, 51010 Tartu, Estonia;13. Vienna BioCenter Core Facilities, Campus-Vienna-BioCenter 1, 1030 Vienna, Austria;14. Department of Pure and Applied Chemistry, University of Strathclyde, 295 Cathedral Street, G1 1XL Glasgow, UK;15. Department of Medical Genetics, Life Science Institute, University of British Columbia, C201 - 4500 Oak Street, V6H 3N1 Vancouver, BC, Canada
Abstract:
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  • Keywords:PYROXD1  oxidoreductase  myopathy  tRNA ligase complex  RtcB  oxidative stress  metalloenzyme  copper  NADPH  NADH  UPR  pre-tRNA splicing
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