烟雾病5 例临床分析

目的:研究烟雾病(moyamoya disease,MMD)的临床及影像学特征。方法:回顾性分析5例烟雾病患者,分析其临床及影像学特点。结果:本组病例既往均无阳性病史,中、青年起病,男性居多,均以缺血性脑血管病起病,肢体瘫痪不重,经颅多普勒(TCD)及头颅核磁改变明显,数字减影血管造影(DSA)检查均存在血管闭塞及侧支开放,烟雾血管网形成,1例MRA证实烟雾血管网形成。结论:对于无既往史的中、青年脑卒中患者,要考虑MMD的可能,需完善TCD、头核磁检寻找证据,最后完善数字减影血管造影确诊。

Clinical Analysis of 5 Cases of Moyamoya Disease

Objective: To study the clinical and radiological features of the moyamoya disease (moyamoya disease, MMD). Methods: We retrospectively analysed 5 cases of moyamoya disease, and observed the clinical and radiographic features of the patients. Results: All cases for medium or youth onset, male predominance, all with ischemic cerebrovascular disease onset, hemiparesis, not heavy, head MRI and TCD change significantly. 5 patients with DSA check there are occlusion of the blood vessel and collateral open, smoke vessels network forming. 1 case confirmed with MRA .Conclusions: The middle-aged and young stroke patients without past history should be confirmed as MMD by improving the TCD, head magnetic resonance imaging examination and digital subtraction angiography.