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Proteostasis deregulation as a driver of C9ORF72 pathogenesis
Authors:Paulina Torres  Felipe Cabral-Miranda  Vicente Gonzalez-Teuber  Claudio Hetz
Affiliation:1. Biomedical Neuroscience Institute (BNI), Faculty of Medicine, University of Chile, Santiago, Chile

FONDAP Center for Geroscience, Brain Health, and Metabolism (GERO), Santiago, Chile

Program of Cellular and Molecular Biology, Institute of Biomedical Science, University of Chile, Santiago, Chile;2. Instituto de Ciências Biomédicas, Universidade do Rio de Janeiro, Rio de Janeiro, Brazil;3. Biomedical Neuroscience Institute (BNI), Faculty of Medicine, University of Chile, Santiago, Chile

Abstract:
Keywords:ALS  C9ORF72  ER stress  FTD  ISR  proteostasis  UPR
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