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Augmented Reticular Thalamic Bursting and Seizures in Scn1a-Dravet Syndrome
Authors:Stefanie Ritter-Makinson  Alexandra Clemente-Perez  Bryan Higashikubo  Frances S Cho  Stephanie S Holden  Eric Bennett  Ana Chkaidze  Oscar HJ Eelkman Rooda  Marie-Coralie Cornet  Freek E Hoebeek  Kazuhiro Yamakawa  Maria Roberta Cilio  Bruno Delord  Jeanne T Paz
Institution:1. Gladstone Institute of Neurological Disease, San Francisco, San Francisco, CA 94158, USA;2. Department of Neurology, University of California, San Francisco, San Francisco, CA 94158, USA;3. Department of Physiology, University of California, San Francisco, San Francisco, CA 94158, USA;4. Neurosciences Graduate Program, University of California, San Francisco, San Francisco, CA 94158, USA;5. Department of Neuroscience, Erasmus MC, Rotterdam, the Netherlands;6. Department of Neurosurgery, Erasmus MC, Rotterdam, the Netherlands;7. Department of Pediatrics, University of California, San Francisco, San Francisco, CA 94158, USA;8. Department of Pediatrics, Catholic University of Louvain, Louvain, Belgium;9. NIDOD Institute, Wilhelmina Children’s Hospital, University Medical Center Utrecht and Brain Center Rudolf Magnus, Utrecht, the Netherlands;10. Laboratory for Neurogenetics, RIKEN Brain Science Institute, Wako, Japan;11. Institut des Systèmes Intelligents et de Robotique (ISIR), Sorbonne University, 4 Place Jussieu, 75005 Paris, France;12. Kavli Institute for Fundamental Neuroscience, University of California, San Francisco, San Francisco, CA 94158, USA
Abstract:
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  • Keywords:Nav1  1  SK current  reticular thalamic nucleus  thalamocortical circuits  thalamocortical oscillations  Dravet syndrome  epilepsy  seizures  optogenetics
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