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Hyperphosphorylation of Glucosyl C6 Carbons and Altered Structure of Glycogen in the Neurodegenerative Epilepsy Lafora Disease
Authors:Felix Nitschke  Peixiang Wang  Peter Schmieder  Jean-Marie Girard  Donald E Awrey  Tony Wang  Johan Israelian  XiaoChu Zhao  Julie Turnbull  Matthias Heydenreich  Erich Kleinpeter  Martin Steup  Berge A Minassian
Institution:1. Institute of Biochemistry and Biology, University of Potsdam, Karl-Liebknecht-Strasse 24–25, 14476 Potsdam-Golm, Germany;2. Institute of Chemistry, University of Potsdam, Karl-Liebknecht-Strasse 24–25, 14476 Potsdam-Golm, Germany;3. Program in Genetics and Genome Biology, The Hospital for Sick Children, 555 University Avenue, Toronto, ON M5G 1X8, Canada;4. Division of Neurology, Department of Paediatrics, The Hospital for Sick Children, 555 University Avenue, Toronto, ON M5G 1X8, Canada;5. Leibniz-Institute of Molecular Pharmacology, Campus Berlin-Buch, Robert-Roessle-Strasse 10, 13125 Berlin, Germany;6. Campbell Family Institute of Breast Cancer Research, Princess Margaret Hospital, 620 University Avenue, Toronto, ON M5G 2M9, Canada;7. Institute of Medical Sciences, University of Toronto, 1 King’s College Circle, Toronto, ON M5S 1A8, Canada
Abstract:
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